Same Disease, Different Approaches: A Report on Six Lymphoma Cases with Extranodal Marginal Zones in Rare Sites
Received Date : 06 Oct 2020
Accepted Date : 20 Jan 2021
Available Online : 18 Feb 2021
Doi: 10.37047/jos.2020-79452 - Article's Language: EN
J Oncol Sci. 2021;7(1):34-8
This is an open access article under the CC BY-NC-ND license
Marginal zone lymphoma (MZL) is a heterogeneous disease with the most common form being extranodal marginal zone lymphoma (EMZL). It mostly involves the glandular epithelial surfaces such as the stomach, ocular adnexa, lacrimal and salivary glands, thyroid, breast, and lungs. Gastric and ocular adnexal EMZL are related to specific infectious agents and can be treated with antibiotics especially during the early stages. Surgery, radiotherapy, rituximab, rituximab with chemotherapy, and observation are the other approaches available for the treatment of EMZL. Here, we presented several cases of EMZL with varying stages of involvements of rather extraordinary tissues along with our systemic treatment approaches. Additionally, we have also described the successful implementation of local treatment options.
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